大分類:血小板
小分類:疾患
解説
(病態・病因)図表
参考文献
1) Fujimura Y, Matsumoto M, Yagi H, Yoshioka A, Matsui T, Titani K: Von Willebrand factor-cleaving protease and Upshaw-Schulman syndrome. International journal of hematology75(1): 25-34. Epub 2002/02/15.
2) Mise K, Ubara Y, Matsumoto M, Sumida K, Hiramatsu R, Hasegawa E, et al: Long term follow up of congenital thrombotic thrombocytopenic purpura (Upshaw-Schulman syndrome) on hemodialysis for 19 years: a case report. BMC nephrology 14: 156, 2013, Epub 2013/07/23.
引用文献
1) Schulman I, Pierce M, Lukens A, Currimbhoy Z: Studies on thrombopoiesis. I. A factor in normal human plasma required for platelet production; chronic thrombocytopenia due to its deficiency. Blood 16:943-57, Epub 1960/07/01.
2) Upshaw JD, Jr: Congenital deficiency of a factor in normal plasma that reverses microangiopathic hemolysis and thrombocytopenia. The New England journal of medicine 298(24): 1350-1352, Epub 1978/06/15.
3) Moake JL, Rudy CK, Troll JH, Weinstein MJ, Colannino NM, Azocar J, et al: Unusually large plasma factor VIII:von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura. The New England journal of medicine 307(23): 1432-1435, Epub 1982/12/02.
4) Furlan M, Robles R, Solenthaler M, Wassmer M, Sandoz P, Lammle B: Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura. Blood 89(9): 3097-3103, Epub 1997/05/01.
5) Kinoshita S, Yoshioka A, Park YD, Ishizashi H, Konno M, Funato M, et al: Upshaw-Schulman syndrome revisited: a concept of congenital thrombotic thrombocytopenic purpura. International journal of hematology 74(1):101-108, Epub 2001/09/04.
6) Levy GG, Nichols WC, Lian EC, Foroud T, McClintick JN, McGee BM, et al: Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura. Nature 413(6855):488-94, Epub 2001/10/05.
著者
藤村 吉博 (奈良県立医科大学 名誉教授(現 日本赤十字社近畿ブロック血液センター所長))
関連用語